Rehabilitación pulmonar en pacientes con diagnóstico de fibrosis quística
DOI:
https://doi.org/10.28957/rcmfr.375Palabras clave:
Rehabilitación, ejercicio, fibrosis quísticaResumen
La fibrosis quística (FQ) es una enfermedad genética que se hereda de forma autosómica recesiva, tiene características multiorgánicas y se presenta con mayor frecuencia en población caucásica. La disfunción respiratoria es la causa de muerte en cerca del 95% de los pacientes con FQ y una causa importante de morbilidad. Los programas de rehabilitación pulmonar en casos de FQ deben centrarse en las necesidades específicas de cada paciente, mejorar su tolerancia al ejercicio y su movilización de secreciones, disminuir el riesgo de complicaciones e impactar en su calidad de vida.
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Derechos de autor 2023 Revista Colombiana de Medicina Física y Rehabilitación
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